blue rubber bullous nevus
Introduction
Introduction Blue rubber bleb nerus syndrome: refers to the cavernous or capillary hemangioma present in both the skin and the gastrointestinal tract. This syndrome is rare and is characterized by the simultaneous occurrence of skin and digestive tract. Spongiform or capillary hemangioma, the tumor appears as blue spotted. If a rupture occurs, it can cause bleeding. Intrinsic is caused by embryonic differentiation and developmental disorders, and is an autosomal dominant hereditary disease. Affects important vital organs and blocks tubular structures such as the intestines, trachea, etc.
Cause
Cause
Intrinsic is caused by embryonic differentiation and developmental disorders, and is an autosomal dominant hereditary disease. There are 3 cases of pathological changes in the skin or digestive tract:
1. Large cavernous hemangioma replaces normal tissue, affects vital organs and blocks tubular structures such as the intestines, trachea, and the like.
2. The blood sac is a blue rubber-like nipple that covers the thin layer of skin.
3. Irregular blue spots, sometimes in the form of spots, invading the surrounding normal skin, and thus various pigment changes from blue-black, blue, and light blue to normal skin color. Histological examination is a capillary or cavernous hemangioma with smooth muscle fibers between the walls and most sweat glands near the blood vessels.
Examine
an examination
Related inspection
Physical examination of skin fungus microscopic examination of skin diseases
When diagnosed, anyone with special skin manifestations such as blue spots and gastrointestinal bleeding should think of this disease.
Clinically, patients often have hematemesis, blood in the stool, and rectal bleeding, causing anemia. The skin veins are dilated and appear like a magenta or blue mass, which is soft. Small lesions can be faded after compression, local pain or tenderness, and excessive sweating above the mass.
Diagnosis
Differential diagnosis
Differential diagnosis of blue rubber bullous:
1, pustule: pustule (pustule) is a localized epidermal cavity bulge, containing turbid pus. It originated from the skin and evolved from papular blisters. Pustules vary in size, and there may be inflammatory redness around them. After the shallow pustules dry up, they become purulent and leave no scars. The pustules can form ulcers and leave scars.
2, pigmentation spots: mixed sputum sputum cells and sputum cells nested in the deep layer of the epidermis also in the dermis called mixed sputum. Common central bulge highlights the leather surface, long hair, surrounded by diffuse distribution, different color, unclear boundary, is the boundary composition, the junction from childhood to the skin ,, so the elderly are rare mixed . Both mixed sputum and junction sputum may have malignant changes.
