Congenital venous malformation limb hypertrophy syndrome

Congenital venous malformation of limb hypertrophy syndrome (Klippel-Treacute; naunay syndrome, KTS) is a complex congenital vascular dysplasia. Clinically, it is characterized by triads of deep and / or superficial venous malformations, cutaneous hemangiomas (moles), and excessive growth of bones and soft tissues. A few cases may be accompanied by cavernous hemangiomas of the soft tissue of the limbs and hemangiomas of the internal organs, and individual patients may be complicated by arterial disease.