Idiopathic pulmonary fibrosis in children

Idiopathic pulmonary fibrosis (IPF), also known as idiopathic pulmonary fibrosis, Hamman-Rich syndrome, idiopathic diffuse interstitial fibrosis of the lung, European scholars call it cryptogenic fibrosing alveolitis, which is mostly referred to as fibrosing alveolitis (FA). It is a diffuse progressive pulmonary interstitial fibrosis of unknown cause, which may not be a disease, but only the end stage of chronic interstitial pneumonia caused by multiple reasons. More common in adults, but can also occur in infants and children. Clinically, it is characterized by irritating dry cough, shortness of breath, progressive dyspnea, and hypoxemia. The condition often continues to progress, eventually dying from respiratory failure.