Orbital bone fibrous dysplasia

Fibrous dysplasia is a kind of self-limited congenital benign bone fibrous tissue disease with unknown etiology and slowly progressing. It is a disease in which normal bone tissue is gradually replaced by hyperplastic fibrous tissue. The disease can be mono- or bony (involving more than 2 bones). It is considered a structural malformation, which is characterized by normal bone tissue being absorbed and fibrous tissue and dysplastic reticular bone. Replaced by trabecular. This disease is not uncommon clinically, accounting for about 25% of new bones, and it is rare in the orbit. However, the disease mostly invades the periorbital bone, causing secondary changes such as shrinkage of the orbital cavity volume and clinical symptoms. Lesions grow slowly, and most of them stop growing after puberty. If the skeletal system is accompanied by skin pigmentation and / or endocrine disorders, it is called Albright syndrome.