Progressive dysplasia of the backbone

This disease is also known as Engelmann disease, diaphyseal sclerosis and camurati-Engelmann-Ribbing disease. It is characterized by spindle-like enlargement and sclerosis of long bone backbone symmetry. This disease is rare. Some people count slightly more men than women. The average age of onset is 19.2 years, ranging from March to 57 years. Involved long bones are the tibia, femur, fibula, humerus, ulna and radius, hands and feet, and the skull is also a common site.