Choroid disease

Choroideremia is also known as total choroidal vascular atrophy or progressive choroidal atrophy or progressive tapetochorordal atrophy. First reported by Mauthner in 1872. The initial manifestations of the fundus were observed to be different from those of primary retinal degeneration, which was considered to be a loss of choroid. After long-term observation, it is found that the choroid and pigment epithelium are not congenital dysplasia, but progressive disappearance. It is also called progressive RPE dystrophy or progressive RPE choroidal degeneration, but it is still customary to continue to use choroidal disease. It is characterized by progressive onset of both eyes, night blindness from childhood, diffuse full-layer choroidal capillaries and RPE atrophy, and finally the choroid completely disappears.