Sturge-Weber syndrome

This disease is also known as encephalotrigeminal angiomatosis, which was first described by Schiremer. Later, Sturge and Weber made detailed reports successively, so the name Sturge-Weber syndrome is Sturge-Weber syndrome. It is the only phacoma-toses with no genetic predisposition, a developmental disease of vascular malformations of the head and face. It is characterized by trigeminal nerve distribution in the face area with skin and mucosal capillary hemangiomas, sometimes with intracranial hemangiomas or invading the eye.